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Recommendations regarding splenectomy in hereditary hemolytic anemias

Subnetwork: Bone marrow failure,Red blood cell defects

Disease group/s: Alpha- thalassaemia diseases,Beta-thalassemia and related diseases,Congenital dyserythropoietic anemia,Hereditary elliptocytosis,Hereditary spherocytosis,Hereditary stomatocytosis,Rare constitutional hemolytic anemia due to pyruvate kinase deficiency,Rare constitutional hemolytic anemia due to an enzyme disorder (Other than PKD),Sickle cell disease and related diseases

Scope and Purpose: 3. Treatment

Patients' involvement?: No

Rigour of development: A - Evidence and consensus based

Link: https://www.ncbi.nlm.nih.gov/pubmed/28550188